What is Idiopathic Pulmonary Fibrosis (IPF)?

What is Idiopathic Pulmonary Fibrosis (IPF)?


Hello, in this HealthSketch we want to talk to you
about Idiopathic Pulmonary Fibrosis or ‘IPF’ The word ’Idiopathic’ means the
cause of the condition is unknown, ‘pulmonary’ means lungs and
‘fibrosis’ means scarring So IPF is a progressive, scarring lung
condition, the cause of which is not known. Though the condition is not well known, It affects around 5 million people worldwide and it usually occurs after the age of 50. While IPF has no known cause it is thought that there may be certain triggers
that cause the scarring process to begin such as: viral infections, smoking, and heartburn. It can also run in families There is no known cure as yet,
however there are things that people with IPF can do to help themselves. So, how does IPF affect the lungs? First, let’s see how the lungs work. When you breathe in, the air ends up
in tiny air sacs called alveoli where oxygen can move into the bloodstream
and carbon dioxide gets taken out. In pulmonary fibrosis, scar tissue builds up
over time around these air sacs, which makes it harder for oxygen
to move into the body This leaves you feeling more
short of breath than usual. The main symptoms of this condition
are breathlessness and a persistent dry cough which both worsen over time,
making daily activities harder. Tiredness, weakness, and weight loss may follow. Diagnosing IPF can be difficult as its
symptoms are often similar to other more common lung conditions. However, if your doctor suspects
IPF from your symptoms, you should be referred to a specialist for further
investigations, such as breathing tests A high resolution CT scan, which takes very
detailed images of the lungs, is used both for diagnosis
and monitoring the condition Another test involves passing a small camera
through your nose or mouth and into your lungs to see what they look
like or take a sample This is called bronchoscopy Another test involves a small operation
under general anaesthetic to take a small sample of tissue for analysis,
which is called a lung biopsy. Unfortunately, there is not yet a treatment that
can cure idiopathic pulmonary fibrosis, but there are now medications that can help
to reduce the symptoms and slow the progress of the condition Research into new drugs is ongoing. Pulmonary Rehabilitation has also been shown
to benefit people with IPF. This is a structured programme of
gentle exercises and education about your condition and how
best to manage the symptoms. Physiotherapists and specialist nurses can show
you techniques to reduce breathlessness. Oxygen therapy can be used if your body’s
oxygen levels become too low, perhaps needed only during physical activity or maybe while at rest too A lung transplant can be an option for those
physically fit enough to undergo major transplant surgery. The progress of the condition varies
widely in different people; while some may have stable symptoms
for long periods, in others there is a gradual decline
with worsening symptoms. Coming to terms with a diagnosis of IPF
is often difficult and it is particularly hard as the cause
of the condition is unclear It is common to feel low, anxious or depressed and it can be helpful to talk about these
feelings with your doctor, a counsellor, or at a support group where there will be others
with similar questions, experiences and feelings. Having the support of others can help to motivate
people with IPF to stay as healthy as possible, for example, by attending follow up appointments,
taking medication as prescribed, and being vaccinated against flu and pneumonia. Stopping smoking is very important, as smoking damages the lungs and worsens
the symptoms of IPF. It’s also good to stay physically active and eating healthily can
make a significant difference by ensuring your body gets the
energy and nutrients it needs. In this HealthSketch we’ve talked about
Idiopathic Pulmonary Fibrosis, the scarring process in the lungs,
the resulting symptoms, and how to cope with the diagnosis
and stay as healthy as possible. We hope this HealthSketch has been helpful
to you and those around you HealthSketch. Health for all to see

8 Replies to “What is Idiopathic Pulmonary Fibrosis (IPF)?”

  1. Early evidence of efficacy of PBI-4050 alone and also in combination with one of the commercially available IPF drugs
    PBI-4050 shown to be very well tolerated whether used alone or in combination with nintedanib or pirfenidone
    LAVAL, QC, Nov. 17, 2016 /CNW Telbec/ – ProMetic Life Sciences Inc. (TSX: PLI) (OTCQX: PFSCF) ("ProMetic" or the "Corporation") announced today positive interim results from its Open Label Phase 2 clinical trial in patients suffering from idiopathic pulmonary fibrosis ("IPF"). In addition to demonstrating that PBI-4050 is safe and well tolerated in patients suffering from IPF, the objective of this study was to provide early evidence of clinical benefits of PBI-4050 treatment whether used alone or in addition to either nintedanib or pirfenidone. Forty patients are enrolled in the study in 6 sites across Canada. At this time, the Corporation is reporting on the first 30 patients that have completed their 12 weeks of treatment.

    "We are very pleased with the results to date from this study as they provide us with very important data points relating to efficacy and safety" stated Dr. John Moran, Chief Medical Officer of ProMetic. "There is early evidence of efficacy in the patients treated with PBI-4050 alone and in those treated with PBI-4050 in combination with one of the commercially available drugs. This compares favourably to that of the pirfenidone or nintedanib treatment reported in the ASCEND trial and in the two INPULSIS trials, respectively. Further good news is the fact that PBI-4050 is very well tolerated by IPF patients whether used alone or in combination with either nintedanib or pirfenidone" added Dr. Moran.

  2. My grandmother never smoked and was very healthy. She got diagnosed with this disease in 2010 when she was 62. She passed away a month ago on April 19 at 68 because of it.

  3. I  suffered deeply with stage four sarcoidosis which  progressed to pulmonary fibrosis. I was hospitalized 18 times in three years, mostly with flare ups and pneumonia. For me, the chronic widespread pain takes my breath away more than the disease itself. At times the pain is so severe I find it difficult to do anything, i was online to know more about this illness when i came across a blog https://curetoidiopathicpulmonaryfibrosis.blogspot.com i contacted the Doctor on his email address at dr.georgetom @ gmail.com,i purchased his herbal medicine called malva-h, after using the product for two months all the pain was gone and breathing became easy after much checkup and examination i was confirm PF free, i advise that if you have similar problem contact DR.GEORGE to enabled you to navigate through this dangerous, painful and mysterious disease. May God embrace you with his gentle comfort, wisdom, and relief. Sincerely.

  4. There’s a potential cure for Idiopathic Pulmonary Fibrosis (IPF).

    The fibrosis is likely caused over several years as the immune system continually repairs lung inflammation caused by large glucose fluctuations resulting from Metabolic Syndrome or Type 2 Diabetes. To cure IPF you have to cure the Metabolic Syndrome or Type 2 Diabetes using a Ketogenic Diet combined with Intermittent Fasting.

    I cured my T2D. See:
    https://youtu.be/JUuHrBwsJ2s

  5. I keep coughing up stomach acid with tiny bits and pieces of food and it tastes awful but I can feel it in my lungs and I have been having severe chest pains and the doctors can't figure out what is causing the pains

Add a Comment

Your email address will not be published. Required fields are marked *